Forschung & Innovation
Publikationen
The Inflammation in the Cytopathology of Patients With Mucopolysaccharidoses- Immunomodulatory Drugs as an Approach to Therapy.
PMU Autor*innen
Anna Maria Wiesinger, Tobias Moser, Florian Lagler
Alle Autor*innen
Anna Maria Wiesinger, Brian Bigger, Roberto Giugliani, Maurizio Scarpa, Tobias Moser, Christina Lampe, Christoph Kampmann, Florian Lagler
Fachzeitschrift
FRONTIERS IN PHARMACOLOGY
Kurzfassung
Keywords
MOUSE MODEL, TARGETED DISRUPTION, OXIDATIVE STRESS, MITOCHONDRIAL DYSFUNCTION, ENZYME REPLACEMENT THERAPY, LYSOSOMAL MEMBRANE PERMEABILIZATION, SULFATE DERIVED DISACCHARIDES, HEPARAN-SULFATE, SANFILIPPO-SYNDROME, KERATAN SULFATE